Kev Ntshav Liab Ntawm Lub Cev Ntshav

Aug 21, 2020

⒈ Kev kuaj pom tseem ceeb ntawm cov qe ntshav liab permeability

⑴ Cov ntshav qe ntshav ntau osmotic fragility tau pom hauv: kab mob txha caj qaum, kab mob autoimmune hemolytic anemia nrog kab mob spherocytosis, thiab lwm yam.

⑵ Txo cov kabmob ntshav liab osmotic fragility tau pom hauv: cov ntshav tsis muaj peev xwm ua haujlwm ntshav, ntshav khov tsis txaus ntshav liab, ntshav ntau dhau los.

⒉ Pom qhov tseem ceeb ntawm cov ntshav liab tsim muaj ntshav tsis zoo osmotic fragility test Qhov kev ntsuas no yog rhiab rau kev kuaj pom qhov sib txawv me me spherocytosis, thiab tseem pom muaj pyruvate kinase deficiency thiab lwm yam enzyme-tsis txaus hemolytic anemia.

Kev ntsuas tseem ceeb ntawm cov khoom kuaj ntshav thiab kuaj ntsuas qhov tseeb

Red Hereditary spherocytosis, hemolysis zoo dua nyob rau hauv hypotonic saline, hemolysis kho tau zoo tom qab ntxiv piam thaj, thiab hemolysis tseem ceeb dua tom qab ntxiv ATP.

⑵ Congenital non-spherical cell hemolytic anemia hom I (G-6-PD tsis txaus), ib txwm los yog kho me ntsis ntawm hemolysis hauv hypotonic saline, hemolysis yog kho tau qee feem tom qab cov piam thaj ntxiv, thiab hemolysis kho qee qhov kho tom qab ATP ntxiv.

⑶ Congenital non-spherical cell hemolytic anemia type II (PK deficiency), hemolysis nyob hauv hypotonic saline pab tau zoo, hemolysis tsis tuaj yeem kho tau tom qab tau ntxiv cov piam thaj, hemolysis tseem ceeb dua tom qab ATP ntxiv.

Leej niam twg thiaj yug tau cov me nyuam uas muaj ntshav ABO sib xws?

1. Hauv keeb kwm kev kho mob, muaj keeb kwm txog kev rho menyuam raug mob thiab muaj keeb kwm muaj lub cev nqaij daim tawv nyob rau hauv tus menyuam yav dhau los.

2. Cov ntshav xyuas yog hom O, thiab tus txiv yog A, B lossis AB hom.

3. Cia siab tias cov niam uas muaj hom ntshav O nrhiav tau cov uas muaj tus kab mob anti-A lossis anti-B ntau dua ua ntej cev xeeb tub.

4. Cov tshuaj tiv thaiv A (B) IgG titer ntawm cov niam cev xeeb tub uas muaj hom O ntshav> 1: 64 thaum cev xeeb tub.

5. Kev kuaj B-ultrasound thaum cev xeeb tub, mob loj heev ntawm daim tawv nqaij tuaj yeem tuaj yeem qhia cov tawv nqaij hauv plab me nyuam, kab mob hepatosplenomegaly thiab lwm yam.


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